Ebstein's anomaly

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Definition

By Mayo Clinic staff

Ebstein's anomaly is a rare heart defect that's present at birth (congenital). In Ebstein's anomaly, your tricuspid valve — the valve between the chambers on the right side of your heart — doesn't work properly. Blood leaks back through the valve, making your heart work less efficiently. Ebstein's anomaly may also lead to enlargement of the heart or heart failure.

If you have no signs or symptoms of Ebstein's anomaly, careful monitoring of your heart may be all that's necessary. If signs and symptoms become troublesome, or if the heart is enlarging or becoming weaker, treatment for Ebstein's anomaly may be necessary. Treatment options include medications and surgery.

References
  1. Attenhofer Jost CH, et al. Ebstein's anomaly. Circulation. 2007;115(2):277-285.
  2. Pflaumer A, et al. Symptomatic neonates with Ebstein anomaly. Journal of Thoracic and Cardiovascular Surgery. 2004;127(4):1208-1209.
  3. Kapusta L, et al. Ebstein's anomaly: Factors associated with death in childhood and adolescence: A multi-centre, long-term study. European Heart Journal. 2007;28(21):2661-2666.
  4. Brown ML, et al. Functional status after operation for Ebstein anomaly: The Mayo Clinic experience. Journal of the American College of Cardiology. 2008;52(6):460-466.
  5. Chen JM, et al. Early and medium-term results for repair of Ebstein anomaly. Journal of Thoracic and Cardiovascular Surgery. 2004;127(4):990-999.
  6. Palmen M. Long-term follow-up after repair of Ebstein's anomaly. European Journal of Cardio-Thoracic Surgery. 2008;34(1):48-54.  
  7. Agarwala BN, et al. Ebstein's anomaly of the tricuspid valve. http://www.uptodate.com/index. Accessed Sept. 29, 2008.
  8. Ebstein's anomaly. American Heart Association. http://www.americanheart.org/presenter.jhtml?identifier=11075. Accessed Oct. 2, 2008.

DS00805

Oct. 31, 2008

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